小肠罕见肿瘤的CT造影特征表现及分析-东南大学学报医学版

小肠罕见肿瘤的CT造影特征表现及分析

单位：南京大学医学院附属鼓楼医院医学影像科, 江苏南京 210008

关键词：小肠肿瘤恶性胃肠道神经外胚叶肿瘤弥漫性神经节细胞瘤病侵袭性血管黏液瘤 CT小肠造影

分类号：R735.32;R739.4

出版年·卷·期（页码）：2022·41·第一期（56-62）

摘要：

目的：分析小肠罕见肿瘤的CT造影表现及其相关临床特征，提高对其的认识和诊断水平。方法：回顾性分析3例经病理确诊的小肠罕见肿瘤的临床以及肠CT造影资料和特征。结果：恶性胃肠道神经外胚叶肿瘤CT造影表现为空肠管壁的不规则增厚，形成类似软组织肿块样的结构，生长方式凸向肠管腔外，增强后呈不均匀强化。回肠弥漫性神经节细胞瘤病CT造影表现为整个回肠管壁连续弥漫性增厚，肠系膜黏膜下见弥漫性结节，管腔多发狭窄，黏膜层明显强化。侵袭性血管黏液瘤CT造影表现为回肠末端囊实性肿块，增强后囊性成分可见轻度强化，边缘强化为著，其内散在细条状强化。结论：小肠罕见肿瘤具有一定的小肠CT造影特点，有助于鉴别诊断。

Objective: To analyze the computed tomography enterography imaging features and clinical features of rare small intestinal neoplasm, and to improve the understanding and diagnosis of them. Methods: Characteristics of the clinic and CT-enterography of 3 cases of rare small intestinal neoplasms confirmed by pathology were analyzed retrospectively. Results: CT imaging of malignant gastrointestinal neuroectodermal tumor showed irregular thickening of jejunum wall, forming a structure similar to soft tissue mass, and the growth pattern protruding out of the lumen. After enhancement, the enhancement was uneven. CT imaging of diffuse ganglioneurosis of the ileum showed continuous diffuse thickening of the entire ileal wall, diffuse nodules under the mesenteric mucosa, multiple lumen strictures, and obvious enhancement of the mucosal layer. Aggressive angiomyxoma presented on CT as a cystic solid mass at the end of the ileum. After enhancement, slight enhancement of the cystic components can be seen, especially at the margins, with scattered thin striated enhancement. Conclusion: The rare small intestinal neoplasms have certain characteristics of small intestinal CT enterography, which are helpful for differential diagnosis.

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